Double uteri with cervicovaginal agenesis

Abstract

To report results of managing complex malformation of the genital tract and to validate a newer classification (vaginal, cervix, uterus, adnexa-associated malformation [VCUAM]) for describing such complex anomalies. Case report. University hospital. A patient with complex genital malformation. Laparotomy, double hysterectomy, and vaginal reconstruction with use of bilateral neurovascular pudendal thigh flaps. Use of VCUAM classification for description of the anatomy of malformation. Creation of a neovagina and accurate and complete description of the anomaly. Relief of pelvic pain and creation of patent and sensate vagina retaining the innervations of the erogenous zones. The VCUAM classification could accurately depict complex anatomic variations. Vaginal reconstruction with use of bilateral neurovascular pudendal thigh flaps yields good postoperative results. The VCUAM classification reflects anatomic variations in external and internal organs precisely.