Double-Outlet Left Ventricle with l-Malposition of the Great Arteries and Subpulmonary Ventricular Septal Defect

Abstract

In a recent issue of your journal we read the interesting report on an infant with ‘‘Double-outlet left ventricle with L-malposition of the great arteries and subpulmonary ventricular septal defect’’ [6]. The authors suggested that ‘‘this anatomic variation has not been described to date in patients with a double outlet left ventricle’’, this may be indeed a rare finding, however, it has been reported in the literature in at least three occasions in children with double outlet left ventricle [2–4]. In subjects with double outlet left ventricle the L-position of the aorta (i.e. the aorta anterior and left sided) is a well known anatomic pattern in which the ventricular septal defect is usually in subaortic position [1, 5]. However in some rare cases of double outlet left ventricle, the Lposition of the aorta can be associated with a subpulmonary ventricular septal defect as clearly showed by two-dimensional echocardiography in the present paper [6] and in the previous reports since 1992 [2, 3]. References