Doença de Kawasaki com acometimento hepático: relato de caso de um paciente com síndrome colestática

Abstract

Kawasaki disease (KD) is characterized by vasculitis in medium-caliber arteries, mainly in children under 5-years-old. The diagnosis should be made by clinical criteria, since there is no specific laboratory test. However, some laboratory and histopathological findings may help to corroborate the diagnosis, especially in inconclusive cases. The objective of this study is to report a case of a patient with a classic DK, who developed cholestatic syndrome and lymphadenopathy, requiring laboratory and pathological investigations (lymph node and hepatic biopsies) to rule out other etiologies. The clinical case described in this study exemplifies how complementary investigation can be used to rule out other etiologies and contribute to the early diagnosis and treatment of KD, which may prevent the disease from developing with complications and severe sequelae, such as coronary aneurysms.