Difficult airway challenge in a pediatric patient with Goldenhar syndrome and atrial septal defect for bone anchored hearing aid surgery

Abstract

Goldenhar syndrome is ocular-auriculo-vertebral dysplasia with cardiac, renal, visceral, and facial abnormalities. Presence of craniofacial and vertebral anomalies increases the risk of difficult airway. Here, we present a case report of a child with Goldenhar syndrome and atrial septal defect (ASD) posted for bone anchored hearing aid surgery. The case report highlights a successful awake retrograde intubation under conscious sedation and topical airway anesthesia, in an 11-year-old child with Goldenhar syndrome and ASD.