Diagnostic and therapeutic strategies of congenital pulmonary sequestration in children

Abstract

pulmonary sequestration (PS) is a rare and serious malformation of the bronchial-pulmonary.It is often associated with cardiovascular dysplasia and diaphragmatic malformations.The most common manifestation of the disease of the lung at newborn and early infancy is respiratory distress.Later on in life, cysts usually lose this compressive character and may remain asymptomatic until infection occurs, while producing cough, fever, and thoracic pain.It also can cause severe cardiovascular and pulmonary symptoms such as dyspnea, heart failure, pleural effusion, hemothorax and hemoptysis.Its symptoms are non-specific characteristic and are easily to be misdiagnosed or missed diagnosis.Misdiagnosis of PS resulted in unnecessary treatments as well as recurrent infectious complications.For confirmation of the diagnosis need imaging procedures such as CT or magnetic resonance angiography to delineate aberrant blood apply.All PS should be treatment because of the risk of infection and interference with lung growth even in asymptomatic patients.The classical therapeutic approach is surgical resection.Embolization of abnormal supply vessels also is effective and safe treatment for PS. Key words: Pulmonary sequestration; Diagnosis; Treatment; Child