Diagnosis and treatment of two girls with congenital H-type rectovestibular fistula and normal anus: Case reports and literature review

Mehmet Hanifi Okur,Suat Cal,Selcuk Otcu

doi:10.14534/j-pucr.2018542546

Abstract

Congenital H-type rectovestibular ﬁstula with normal anus is a rare form of anorectal malformations. In the diagnosis of a female patient with H-type fistula, history may have an important role, creating a high degree of suspicion and calling for direct careful examination of the vestibule. There is also no consensus on the optimal treatment of this rare anomaly. Here, we present the diagnosis, clinical and anatomical features, and treatment results in the cases of two girls who had an H-type fistula with normal anus.

Highlights

Anorectal malformations (ARMs) are common congenital abnormalities that constitute a significant part of proctological childhood diseases
H-type rectovestibular fistula is reported to be 12.5% higher in East Asia and India, there are a small number of ARM cases in North America [1,2,3]
The etiology of H-type fistulas is uncertain, but the condition is generally thought to be congenital in cases associated with H-type ARMs

Summary

Introduction

Anorectal malformations (ARMs) are common congenital abnormalities that constitute a significant part of proctological childhood diseases. Congenital H-type rectovestibular fistula, a rare variant on this spectrum, is found in only 3% of the world’s normal anus cases. H-type rectovestibular fistula is reported to be 12.5% higher in East Asia and India, there are a small number of ARM cases in North America [1,2,3]. We present the diagnosis, clinical and anatomical features, and treatment results in the cases of two girls who had an H-type fistula with normal anus.

Results

Conclusion