Diagnosis and treatment of partial anomalous pulmonary venous connection

Abstract

To explore the diagnosis and treatment of partial anomalous pulmonary venous connection (PAPVC). The clinical data of 38 pediatric patients with PAPVC were retrospectively reviewed. All received ultrasonography and part of them received angiography or 64-detector spiral computed tomography. Then the enlarged atrial septal was repaired with patch to separate the pulmonary vein dystopia to left atrium or the vertical vein was anastomosed to left atrium directly or by homograft vessel. The complicating abnormalities were corrected. Follow-up was conducted for 3 months to 7 years. One case died from severe low cardiac output after operation. Two cases were complicated postoperatively with II degree atrial ventricular block and one with pulmonary hypertensive crisis, and all were cured after treatment. And the other patients recovered after surgery. Follow-up showed that the quality of their postoperative life was good and no relapse to obstruction of pulmonary venous was reported. Missed diagnosis always occur in PAPVC, the debauche and blood flow of pulmonary vein should be overviewed carefully during ultrasonographic examination. Transesophageal echocardiography and contrast examination may help. CT and MRI elevate the final diagnosis rate of PAPVC. The result of operation on PAPVC is good.