Abstract
In the most recent publications on Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome, the uterine remnants and ovaries in patients may develop uterine remnant leiomyoma, adenomyosis, or ovarian tumor, and this can lead to problems in differential diagnosis. Here we summarize the diagnosis methods and available interventions for ovarian tumor in MRKH syndrome, with emphasis on the relevant clinical findings and illustrative relevant case. According to the clinical findings and illustrative relevant case, with the help of imaging techniques, ovarian tumors can be detected in the pelvis in patients with MRKH syndrome and evaluated in terms of size. Laparoscopy could further differentiate ovarian tumors into different pathological types. In addition, laparoscopic surgery not only is helpful for the diagnosis of MRKH combined ovarian tumor, but also has a good treatment role for excising ovarian tumor at the same time. Moreover, laparoscopic removals of ovarian tumor can be considered as a safe and reliable treatment for conservative management.
Highlights
The Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome is characterized by congenital hypoplasia of the uterus and the upper part of the vagina
In the most recent publications on MRKH syndrome, we could found some cases report about uterine remnant leiomyoma, or adenomyosis, but the ovarian tumor is rare in MRKH syndrome and is difficult to be diagnosed [3,4,5,6,7,8]
From our illustrative relevant case, we treated a rare case of large ovarian serous papillary cystadenofibroma in a young woman with the MRKH syndrome with laparoscopic surgery
Summary
The Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome is characterized by congenital hypoplasia of the uterus and the upper part of the vagina. In the most recent publications on MRKH syndrome, we could found some cases report about uterine remnant leiomyoma, or adenomyosis, but the ovarian tumor is rare in MRKH syndrome and is difficult to be diagnosed [3,4,5,6,7,8]. Most publications about pelvic masses in MRKH are about uterine remnants, adenomyosis, or fibroids, the occurrence of ovarian tumors in MRKH could not be ignored as these patients do have ovaries. The aim of this review is to describe the diagnosis methods and available interventions for ovarian tumor in Mayer-Rokitansky-Kuster-Hauser (MRKH) Syndrome, with emphasis on the relevant clinical findings and illustrative relevant case
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