Diagnosis and management of inferior vena cava leiomyosarcoma: review of the literature with a case presentation

Abstract

Inferior vena kava (IVK) leiomyosarkomu, nadir gorulen bir hastaliktir. Bu nadir tumorun en iyi tedavisi, tumorun tamamen cerrahi rezeksiyonu ve dolayisiyla venoz rekonstruksiyon ihtiyaci doguran IVK’nin rezeksiyonudur. Rezeksiyon sonrasi IVK’nin baglanmasi veya primer onarim, yama ile onarim veya sentetik ya da biyolojik materyallerle tup greft konulmasi gibi farkli rekonstruksiyon yontemleri mevcuttur. Inferior vena kava leiomyosarkomlarina iliskin mevcut bilgiler olgu sunumlari ve kucuk olgu serilerine ait oldugu icin, olgu sunumlarinin bildirilmesi onemlidir. Bu yazida, IVK leiomyosarkomu olan ve Dacron tup greft ile rekonstruksiyon uygulanan 69 yasinda kadin bir olgu, IVK leiomyosarkomalarinin tanidan tedaviye klinik ozellikleri, literatur verileri esliginde incelenerek sunuldu. Anah tar soz cuk ler: Inferior vena kava; leiomyosarkom; vaskuler tumor. Inferior vena cava (IVC) leiomyosarcoma is a rare clinical entity. The best treatment for this rare tumor is complete surgical resection of the tumor and consequently resection of IVC leading to the need for venous reconstruction. Ligation of IVC after resection or reconstruction including primary repair, patch repair or tube grafting with synthetic or biological materials are available. As the current knowledge of IVC sarcomas is based primarily on case reports and small case series, it is of utmost importance to report individual cases. In this article, we report a 69-yearold female with IVC leiomyosarcoma who underwent reconstruction with a Dacron tube graft in the light of clinical characteristics of the disease from diagnosis to treatment along with a detailed review of the literature data.