Desmoid-type fibromatosis in splenic hilum with rupture of lienal artery aneurism in a 17-year-old male

Abstract

Desmoid Fibromatosis (DF) is locally aggressive benign fibroblastic or myofibroblastic tumor with no metastatic potential, but has high recurrence rate. The symptoms vary according to tumor location, abdominal or extra-abdominal.