Dermatopathia pigmentosa reticularis: a rare case

Abstract

Dermatopathia pigmentosa reticularis (DPR) is a rare ectodermal dysplasia with a triad of generalized reticulate hyperpigmentation, noncicatricial alopecia, and onychodystrophy. We report a case of a 21-year-old man who had generalized reticulate pigmentation, diffuse noncicatricial alopecia, and onychodystrophy of finger and toe nails. Along with this triad, he also had mild atrophy of skin over hands and feet, palms and soles, and loss of dermatoglyphics. There was no evidence of involvement of other organs with ectodermal origin.