Dermatomyositis Presenting as Pseudo-angioedema

Abstract

Dermatomyositis is an autoimmune inflammatory myopathy that has a heterogeneous clinical presentation, which can make it difficult to diagnose. We present the first case report of Wong-type dermatomyositis presenting with pseudo-angioedema. A 65-year-old man presented with several months of facial swelling, dysphagia, and dysarthria. The patient developed a diffuse cutaneous rash, periorbital swelling, and proximal muscle weakness. Skin biopsy was consistent with a diagnosis of Wong-type dermatomyositis.