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Abstract
Introduction: Dermatofibrosarcoma protuberans (DFSP) is an intermediate and slow-growing sarcoma, arising most commonly in the trunk and extremities and rarely in the breast. It may be recurrent, but metastasis is rare. Excision with good resection margins reduces the rate of recurrence. Case Presentation: A 28-year-old lady presented with a painless lump in the left breast of 16 years duration. Examination revealed an ulcerated firm mass, well defined, with perilesional nodules on the skin of the breast. Wedge biopsy favoured Borderline Phylloides Tumour over DFSP. Patient was offered mastectomy and the histology of the specimen confirmed Fibrosarcomatous DFSP. Conclusion: This stresses the importance of histology in diagnosing a rare breast tumour. This is very important because it may show similar appearance to other benign and malignant breast lesions, which makes clear the role of pathological investigation to make a definitive diagnosis.
Highlights
Dermatofibrosarcoma protuberans (DFSP) is an intermediate and slow-growing sarcoma, arising most commonly in the trunk and extremities and rarely in the breast
Patient was offered mastectomy and the histology of the specimen confirmed Fibrosarcomatous DFSP. This stresses the importance of histology in diagnosing a rare breast tumour
In spite of its classification as a tumour of intermediate malignancy with a limited potential for metastasis, DFSP possesses the potential for aggressive local behavior
Summary
Dermatofibrosarcoma protuberans (DFSP) is an intermediate and slow-growing sarcoma, arising most commonly in the trunk and extremities and rarely in the breast. It may be recurrent, but metastasis is rare. Dermatofibrosarcoma Protuberans (DFSP) is a rare tumour involving the deep dermis and subcutaneous tissues. It accounts for 1.0% of all soft tissue sarcomas, and for less than 0.1% of all malignant tumours [1]. The disease can occur at any age, but 20-50 years age group is most commonly affected It is a slow-growing sarcomatous tumour involving the trunk and extremeties [2].
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