Dermatofibrosarcoma protuberans-a rare neoplasm.

Abstract

Dermatofibrosarcoma protuberans (DFSP) is a rare low-grade tumour which accounts for about 6% of all soft tissue sarcoma. It is typically a superficial cutaneous tumour characterized by high rates of local recurrence but with low risk of metastasis (1). In about half of DFSP cases, the tumour is located on the trunk, followed by 30-40% of cases located in the proximal portion of the limbs, and 10-15% of cases in the head and neck (2). Clinical diagnosis can be made based on tumour’s clinical appearance, thus, the role of imaging diagnosis is limited. Despite its superficial location and slow growing feature, large lesions of DFSP may demonstrate deep tissue invasion and atypical manifestations, therefore, resulting in misdiagnosis. Since only several reports are available in the literature with a focus on imaging findings of DFSP (2-6), we report a case of DFSP with the aim of enhancing our knowledge of this unusual tumour.