Dermatofibrosarcoma of Darrier Ferrand Wide Surgical Excision of a Thoracic Location: About a Case and a Review of the Literature

Abstract

Dermatofibrosarcoma (DFS) is a fibrous tumor of the skin, slow growing, with a very high risk of local recurrence, but with a low metastatic potential associated with a specific chromosomal translocation. It is found more frequently in adults and the elderly. The curative treatment is surgical by a wide excision laterally and in depth. This excision results in large losses of substances, the coverage of which is a real challenge for the surgeon and requires different means ranging from skin grafts to free musculo-cutaneous flaps. We report the case of a 49-year-old patient with a voluminous purplish polylobed anterior and upper thoracic mass. The radiological assessment revealed a superficial parietal dermal mass. He had a biopsy confirming the diagnosis of Dermatofibrosarcoma of Darried and Ferrand. The excision surgery allowed a wide and complete resection with directed recovery with excellent postoperative results without recurrence at 06 months. The aim of this article is to present the therapeutic procedure for this pathology taking into account the site of the tumor, the size, the time of occurrence, the number of recurrences, the clinical signs, the operating protocol, the results of the pathological examination and post-operative complications with a review of the literature.