Dermato-fibrosarcome de Darrier-Ferrand de la région inguinale

Abstract

The study involved a 32-year old man in good general condition presenting with slow growth mass progressing over 5 years. Clinical examination showed reddish nodule mass covered of hard consistency crusts measuring 74x52x68 mm in diameter at the level of the right inguinal region and adhering to the deep planes, without superficial lymphadenopathy (A). Magnetic Resonance Imaging showed burgeoning process infiltrating the subcutaneous fat. This was in contact with the muscular plane without involving the external genitalia (B, C). Local biopsy and histological examination with immunostaining confirmed the diagnosis of Darier Ferrand´s dermatofibrosarcoma. In this case, 3-cm surgical excision margin, pedicled anterolateral fasciocutaneous thigh flap reconstruction and thin thickness skin grafting from the donor area (D) were performed. Dermatofibrosarcoma is a mesenchymal tumor arising in the dermis with intermediary malignancy and a high risk of recurrence. This study highlights that 5-cm surgical excision margin is recommended to improve local control after surgery but it is difficult in patients with Darier Ferrand´s dermatofibrosarcoma affecting such an important anatomical region.