Dentin Dysplasia Type I: A Rare Case Report and Management Protocol

Shimasadat Miri,Parisa Soltani,Mahsasadat Miri,Amirhossein Moaddabi

doi:10.12691/ijdsr-5-5-2

Abstract

Dentin Dysplasia (DD) is a rare autosomal dominant anomaly that disturbs the formation of dentin in primary and/or permanent dentitions. This condition is classified into types I (radicular) and II (coronal) based on radiological findings. A case of DD type I in an 11-year old Iranian boy is presented and the clinical and radiological findings and selected treatment plan are discussed.

Highlights

Dentin Dysplasia (DD) is a rare autosomal dominant anomaly that disturbs the formation of dentin either in the primary or both primary and permanent dentitions
DDI is characterized by presence of primary and permanent teeth with morphologically normal or slightly amber colored crown with no or only rudimentary root development, improper growth of dentin resulting in incomplete or total obliteration of the pulp chamber, and periapical radiolucent areas or cysts which can lead to early loss of tooth [5,6,7]
Odontoblasts express specific genes products which form the collagenous dentin extracellular matrix. This matrix consists of mostly type I, type I trimer, type III, type V, and type VI collagens and several noncollagenous proteins found in bone extracellular matrix, such as osteonectin, osteocalcin, osteopontin, bone sialoprotein, and dentin matrix protein 1

Summary

Introduction

Dentin Dysplasia (DD) is a rare autosomal dominant anomaly that disturbs the formation of dentin either in the primary or both primary and permanent dentitions. Prevalence of this condition is reported to be approximately 1 in 100,000 patients [1]. Delayed eruption of teeth is reported in DDI, generally teeth erupt in the normal time [8]. In DDI teeth appear to have greater resistance to caries than normal teeth [9]. The enamel and immediately subjacent dentin appear normal. The present report describes a case of DDI in an 11-year-old boy attending a private office in Iran

Case Report

Discussion

Conclusion