Abstract
Patients with special health care needs (PSHCN) may have an increased risk of oral disease throughout the course of their life and require particular delivery of dental care due to their medical condition or limitations. The purpose is to report the dental management of a patient with Cornelia de Lange Syndrome (CdLS), which was classified as PSHCN due to physical, behavioural, cognitive, and emotional impairment. A 14-year-old female with a clinical diagnosis of CdLS and its common craniofacial features such as microcephaly, short neck, synophrys, arched eyebrows, downturned angle of the mouth, high arched palate, micrognathia, and microdontia was referred to the hospital where the dental treatment was performed under general anesthesia. Multiple tooth extraction, fillings, and coronary polishing were performed. During the follow-up, we observed that dental restorations were clinically satisfactory and there was an improvement in the patient's behaviour during dental treatment. Managing and shaping behaviour of such patients are crucial to delivering quality dental care, as they require specialized care due to their behavioural and clinical conditions.
Highlights
Patients with special health care needs (PSHCN) may have an increased risk of oral disease throughout the course of life [1] and require particular delivery of dental care due to their medical condition and limitations [1, 2]
The most common craniofacial features are microcephaly, short neck with low anterior and posterior hairlines, synophrys, long curly eyelashes, downturned angles of the mouth, high arched palate, micrognathia, macroglossia, microdontia, delayed tooth eruption, and partial anodontia [5, 7,8,9]. The purpose of this case report is to endeavor further guidance for dental practitioners relating to the dental management of patients with Cornelia de Lange Syndrome (CdLS) which is classified as PSHCN due to physical, behavioural, cognitive, and emotional impairment
The management of the patient was difficult due to her aggressive behaviour; after the procedure was performed under general anesthesia, we observed an improvement in the patient’s subsequent behaviour during dental care
Summary
Patients with special health care needs (PSHCN) may have an increased risk of oral disease throughout the course of life [1] and require particular delivery of dental care due to their medical condition and limitations [1, 2]. The most common craniofacial features are microcephaly, short neck with low anterior and posterior hairlines, synophrys, long curly eyelashes, downturned angles of the mouth, high arched palate, micrognathia, macroglossia, microdontia, delayed tooth eruption, and partial anodontia [5, 7,8,9] The purpose of this case report is to endeavor further guidance for dental practitioners relating to the dental management of patients with CdLS which is classified as PSHCN due to physical, behavioural, cognitive, and emotional impairment
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