Delay in diagnosis of Churg–Strauss syndrome: a case report

Abstract

Churg-Strauss syndrome (CSS) is a well established disorder of the blood vessels. However, it is still sometimes not diagnosed early enough to avoid serious complications. It is the later stage that carries the more serious complications. Therefore, we emphasize the ways in which the diagnosis can be made early enough to avoid this stage of the disease. We report a case of CSS that was not diagnosed early and so the patient went on to develop severe cardiac and neurological manifestations. In this report we discuss the techniques and the methods to diagnose CSS and discuss their effectiveness in establishing the diagnosis. We also explore late cardiac and neurological complications because these are particularly serious complications later in the disease. We conclude that the criteria established by the American College of Rheumatology for CSS is the best tool available for early diagnosis and that late stage manifestations of CSS carry high rates of morbidity and mortality.