Abstract
The diffuse cystic lung diseases (DCLDs) are a diverse group of lung disorders characterized by thin-walled parenchymal lucencies with a well-defined interface with normal lung. Emphysema, bronchiectasis, fibrotic lung disease, and cavitary lung diseases can also produce parenchymal lucencies that can mimic true DCLDs. A variety of low-grade or high-grade metastasizing neoplasms, polyclonal or monoclonal lymphoproliferative disorders or plasma cell dyscrasias, infections, autoimmune or connective tissue diseases, smoking-related lung disorders, and congenital or developmental defects can present with DCLD. The operating principle for this book is that the presentation, differential diagnosis, and management for the DCLDs differ from the interstitial lung diseases, and should be classified separately.KeywordsCystDiffuse cystic lung diseases (DCLDs)Lymphangioleiomyomatosis (LAM)Pulmonary Langerhans cell histiocytosis (PLCH)Birt-Hogg-Dubé syndrome (BHD)Lymphoid interstitial pneumonia (LIP)Sjögren syndromeAmyloidosisLight chain deposition disease (LCDD)Malignancy
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