Deaf People with Wardenberg Syndrome Type II: Jordanian Case Study

Abstract

This study aimed to identify deaf people with Deaf with Waardenburg Syndrom Type II. In order to achieve the objectives of the study, the qualitative method was used for the one case study. The sample included (2) deaf students from all deaf schools in Jordan, who are between the ages of (9-10), and (Wechsler Intelligence Scale ,WISC-IV) was applied in the language of Performance Scales and Audiometry. The results of the study showed the presence of symptoms in Deaf people with Wardenberg syndrome type II in terms of: auditory sensory loss. The presence of a side shift to the inner corner of the eyes. Premature graying of hair on the front of the head in white and some on the eyelashes or on the eyebrow. The eyebrows are connected to each other. Dark blue or brown eyes with black and pigment color differences in the iris. The root of the nose is wide and the presence of the rabbit's lip. The results of the study also showed that there is an intense focus during communication in the sign language at the hands of the speaker due to the fact that the color contrast of the eyes led to a dispersion of the focus in the sign language. They also have a sense of the direction of light, which may adversely affect the process of visual communication of sign language. The results of the study also showed that the average hearing impairment was the highest category. The study recommends further studies and research related to the level of intelligence of deaf people with Type II syndrome, as well as studies related to visual perception in Deaf people with type 2 Wardenburg syndrome and the inclusion of this syndrome as an important part of the categories of hearing impairment.