Cutaneous Rosai-Dorfman Disease Recurrence in Nasal Region

Abstract

Rosai-Dorfman disease (RDD), also known as sinus histiocytosis with massive lymphadenopathy, is a benign non-Langerhans cell histiocytic proliferation which was first described in 1969 by Rosai and Dorfman. The disease most commonly involves the lymph nodes but can be seen in virtually any part of the body. The clinical presentation is usually painless massive bilateral cervical lymphadenopathy. The cutaneous form of Rosai-Dorfman disease (CRDD) is a rare entity that manifests solely with skin papules or nodules and it does not present with the usual myriad of symptoms of classical RDD. Here, we report a case of cutaneous RosaiDorfman disease in a 43 year old woman that recurred in the nasal region postoperatively.