Abstract
Bronchogenic cysts are rare developmental anomalies, se en primarily in the pediatric population. Cutaneous manifestations of bronchogenic cysts are still rarer. This lesion poses diagnostic challenge for the clinicians and in almost all, histopathological examination gives the precise diagnosis.We report a case of presternal cystic lesion in 11 year old boy,clinically diagnosed as dermoid cyst, however the lesion was suggestive of cutaneous bronchogenic cyst on histopathology. DOI: 10.21276/APALM.1296
Highlights
Bronchogenic cysts are rare benign congenital developmental anomalies of the ventralforegut.[ 1 ]. They are endodermal cysts and when they are lined by the respiratory epithelium predominantly, it is termed as a bronchogenic cyst.[2]Bronchogenic cysts have a reported prevalence of 1 in 42,000 to 1 in 68,000
In a large series composed of 2,163 cases of mediastinal lesions, 3.3% were foundto be bronchogenic cysts. [3]Unusual sites of presentation include skin, subcutaneous tissue,pericardium and retroperitoneum.[2,4]Under cutaneous location, most common site is the suprasternal notch, followed by presternal area, neck and scapula.[5]
Grey brown toyellow fatty tissue bit was identified which on cut section showed a tiny cyst surrounded by yellow fatty areas.Microscopy revealed a cyst lined by ciliated columnar respiratory epithelium, overlying oedematous fibrocollagenous stroma with occasional mucinous glands, scattered scant lymphocytic infiltrate, muscle fibres ( Massonstrichrome positive) and congested blood vessels overlying fibroadipose stroma (Fig 1,2,3,4)
Summary
Bronchogenic cysts are rare benign congenital developmental anomalies of the ventralforegut.[ 1 ]. [3]Unusual sites of presentation include skin, subcutaneous tissue,pericardium and retroperitoneum.[2,4]Under cutaneous location, most common site is the suprasternal notch, followed by presternal area, neck and scapula.[5]. An 11 year old male child presented to the outpatient department with a swelling over manubrium sterni since birth. Surgical exploration revealed a cystic mass which wascompletely removed and was sent for histopathological examination. Grey brown toyellow fatty tissue bit was identified which on cut section showed a tiny cyst surrounded by yellow fatty areas.Microscopy revealed a cyst lined by ciliated columnar respiratory epithelium, overlying oedematous fibrocollagenous stroma with occasional mucinous glands, scattered scant lymphocytic infiltrate, muscle fibres ( Massonstrichrome positive) and congested blood vessels overlying fibroadipose stroma (Fig 1,2,3,4).
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