Customized hollow surgical stent for congenital vaginal agenesis in early adolescent female with MRKH syndrome: a case report

Abstract

Mayer-Rokitansky-Kuster-Hauser syndrome (MRKH) is a congenital malformation resulting in the absent or small uterus and variable degrees of vaginal hypoplasia of its upper portion. One of the treatment goals for these patients is the creation of an artificial vagina either conservatively or surgically. Use of long-term prosthetic vaginal stents prevents the possible contraction of the reconstructed vagina, maintain vaginal width and depth and avoid vaginal stenosis. Prefabricated stents of standard sizes have widely been utilized to assist surgical creation of a neovagina. However, a customized stent has the evident advantage of the possibility of adjusting the size as per individual patient requirements. In the present clinical report, an early adolescent female patient with MRKH syndrome was surgically managed with insertion of a customized vaginal stent that offers the versatility of design configuration to suit the various clinical situations.