CT Imaging of Craniofacial Fibrous Dysplasia.

Zerrin Unal Erzurumlu,Peruze Celenk,Emel Bulut,Yakup Sancar Barıs

doi:10.1155/2015/134123

Zerrin Unal Erzurumlu, Peruze Celenk + Show 2 more

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https://doi.org/10.1155/2015/134123

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Abstract

Fibrous dysplasia is a benign fibroosseous bone dysplasia that can involve single (monostotic) or multiple (polyostotic) bones. Monostotic form is more frequent in the jaws. It is termed as craniofacial fibrous dysplasia, when it involves, though rarely, adjacent craniofacial bones. A 16-year-old girl consulted for a painless swelling in the right posterior mandible for two years. Panoramic radiography revealed ground-glass ill-defined lesions in the three different regions of the maxilla and mandible. Axial CT scan (bone window) showed multiple lesions involving skull base and facial bones. Despite lesions in the skull base, the patient had no abnormal neurological findings. The lesion was diagnosed as fibrous dysplasia based on radiological and histopathological examination. In this paper, CT findings and differential diagnosis of CFD are discussed. CT is a useful imaging technique for CFD cases.

Highlights

Fibrous dysplasia is a developmental tumor-like disease having characteristics of replacement of normal bone by an excessively proliferated cellular fibrous connective tissue intermixed with irregular bony trabeculae [1]
Radiological, and histopathological examinations, the lesions were diagnosed as craniofacial fibrous dysplasia (CFD)
When the disease is limited to a single bone, it is termed as monostotic fibrous dysplasia

Summary

Introduction

Fibrous dysplasia is a developmental tumor-like disease having characteristics of replacement of normal bone by an excessively proliferated cellular fibrous connective tissue intermixed with irregular bony trabeculae [1]. Fibrous dysplasia (FD) may affect single (monostotic = MFD) or multiple (polyostotic = PFD) bones. Monostotic FD is called CFD when it occurs adjacent to the craniofacial bones. Craniofacial involvement in CFD most commonly results in neurological symptoms like hearing loss, visual loss, headache, proptosis, and so forth [1, 2]. The case presented here was incidentally revealed during the intraoral examination of the patient. Radiological examination showed that several craniofacial bones were affected. CFD was diagnosed with both CT and histopathologic examination

Case Report

Discussion

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