Corrective osteotomy for the treatment of femoral deformity in children with osteogenesis imperfecta

Abstract

Objective To evaluate the surgical strategies and outcomes of multiple corrective osteotomy for the treatment of femoral deformity in children with osteogenesis imperfecta.Methods Between 2004 and 2007,14 femora of 10 patients with osteogenesis imperfect,who underwent recurrent fractures and/or deformities in the femora at this center,were recruited in this study.They included 7 males and 3 females,aged from 5 to 16 years old(mean age,10.3 years old).The femoral deformities were corrected by multiple corrective osteotomy and Rush pins.After surgery,the clinical conditions of these patients regarding mobility status,growth and limb-length,and infection were followed up.Radiological images were taken to monitor pin placement,migration,bending,breakage of pins,and refracture of femora.Results The average duration of follow-up was 3.5 years(ranged from 3 to 5 years).Union was achieved in all cases within 7 weeka(ranged from 6 to 9 weeks).The mean age at primary surgery was 6.1 years old The pin revision surgeries were performed on 4 patients.No complication was noted.Postoperative mobility and lower extremity function were improved in all patients (P<0.01).Conclusions Multiple corrective osteotomy is effective for the treatment of femoral deformity in children with osteogenesis imperfect. Key words: Osteogenesis imperfecta; Lower extremity deformities,congenital; Osteotomy