Abstract
A 7-year-old girl was referred to our department for evaluation of congenital right-sided facial palsy (video on the Neurology ® Web site at [Neurology.org][1]) and bilateral sensorineural deafness (figure 1). On axial MRI, right facial nerve is not visualized in the cerebellopontine angle cistern with bilateral hypoplastic cochlea. On axial high-resolution CT (HRCT), labyrinthine and tympanic segments of the right bony facial canal are thin and hypoplastic. The mastoid segment of right facial canal is absent on coronal HRCT (figure 2). Congenital facial palsy due to facial nerve agenesis is very rare.1 Causes include intrauterine/perinatal trauma and developmental conditions including Möbius syndrome. Unilateral involvement may be secondary to early intrauterine ischemic or traumatic insult. [1]: http://www.neurology.org/
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