Abstract
The development of the respiratory system starts at 3 weeks of gestation, and aberrations in developmental processes may result in structural abnormalities collectively referred to as bronchopulmonary foregut malformations. These lesions include congenital cystic adenomatoid malformations (CCAMs), sequestrations and infantile lobar emphysema. Case presented is of right lung CCAM diagnosed at 23 weeks of gestation, followed during antenatal periods for complications, delivered at 39 weeks, planned thoracotomy with lobectomy done on 3rd day of life and followed up till 1 year. Detailed anomaly scan and close monitoring for structural abnormalities of fetus is needed for appropriate management. Relationship of CPAM with early pregnancy severe infections remains to be established.Med Phoenix Vol.2(1) July 2017, 63-66
Highlights
The respiratory system starts its development from 3rd week of gestation, and aberrations in this development may result in structural abnormalities collectively referred to as bronchopulmonary foregut malformations
It is due to improved antenatal ultrasounds that most congenital pulmonary airway malformations (CPAMs) are diagnosed during antenatal period usually around the time of anomaly scan or can be identified in the neonatal period
Congenital pulmonary airway malformation (CPAM) is a rare developmental abnormality of the lower respiratory tract firstly described as a distinct anomaly by Ch'in and Tang in 1949.2 Many cases are detected by routine prenatal ultrasound examination
Summary
The respiratory system starts its development from 3rd week of gestation, and aberrations in this development may result in structural abnormalities collectively referred to as bronchopulmonary foregut malformations. These lesions include congenital pulmonary airway malformations (CPAMs), sequestrations and infantile lobar emphysema. Congenital pulmonary airway malformation (CPAM) is a rare developmental abnormality of the lower respiratory tract firstly described as a distinct anomaly by Ch'in and Tang in 1949.2 Many cases are detected by routine prenatal ultrasound examination. Klebsiella was responsible organism and UTI was associated with abnormal liver function tests (raised transaminases and ψ glutamyl transpeptidase) MED PHoenix : An Official Journal of NMC, Birgunj, Nepal, Volume (2), Issue (1) July 2017, 63-66
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