Congenital orbital malignant tumor in a neonate: Anesthetic management

Abstract

Neonatal tumors are clinically diagnosed before the first month of life. Some of them are congenital and exist at birth. Since neonatal neoplasms account for 2% of all pediatric tumors, neonatal neoplasms are considered to be rare. Its incidence is estimated to be 2.8-3.74 cases per 100000 newborns per year. Perinatal tumors are different from the tumors commonly found in older children and adults in terms of pathogenesis, behavior, response to treatment, and outcome [1]. The most common neonatal tumors include neuroblastoma, CNS tumors, retinoblastoma, sacrococcygealteratoma, and other rare tumors such as leukemia, renal tumors, and sarcoma [2]. Malignant round cell tumors are extremely malignant and aggressive with poor prognosis. Congenital undifferentiated sarcoma is a subgroup of round cell tumors. It is a rare tumor on which a handful of research studies have been done [3,4]. Its true incidence is largely unknown. We present a rare case of congenital orbital malignant round cell tumor in a neonate and discuss its anesthesia management.