Congenital Granular Cell Tumor – A Rare Entity

Monal Yuwanati,Ashok Mhaske,Shubhangi Mhaske

doi:10.47338/jns.v4.170

Monal Yuwanati, Ashok Mhaske + Show 1 more

Open Access

https://doi.org/10.47338/jns.v4.170

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Abstract

Congenital granular cell tumor is a rare benign neoplastic growth affecting the gingival mucosa of neonates. Prenatal ultrasound diagnosis has recently come to focus and in spite of several reports on immune-histochemical and other advanced marker studies, the cause and origin of the lesion remains debatable till date. Review of literature on prenatal diagnosis and histopathology along with immunohistochemistry is discussed.

Highlights

Congenital Epulis (CE), or congenital granular cell tumour (CGCT), is a congenital benign rare tumour of the newborn
Other terminologies for CGCT described in literature are congenital epulis, granular cell rabdomyoma, congenital myoblastoma, or Neumann’s tumour
It was suggested to be discontinued and congenital granular cell tumour to be used in the literature

Summary

Introduction

Congenital Epulis (CE), or congenital granular cell tumour (CGCT), is a congenital benign rare tumour of the newborn. Other terminologies for CGCT described in literature are congenital epulis, granular cell rabdomyoma, congenital myoblastoma, or Neumann’s tumour. It was suggested to be discontinued and congenital granular cell tumour to be used in the literature. The congenital gingival granular cell tumour is most frequently seen on the alveolar median ridge of the maxilla than alveolar ridge of mandible (1:3). Multiple lesions (10%) has been reported involving either or both jaws and have been described with associated abnormalities of the nasal bridges and septum [13,14,15] It arises from the pre-incisor-canine area [11]. Literature survey has suggested that maxilla as most common site of involvement [Fig. 1]

Prenatal Diagnosis

Differential Diagnosis

More vascularity in a plexiform arrangement

Findings

Conclusion