Congenital giant pigmented nevus

Abstract

Giant congenital pigmented nevi (<1/20,000 births) occur most commonly on the posterior trunk, but may also appear on the head or the extremities. The appearance of pigmented nevi at birth is not common place. Only 3% of infants are in born with visible nevi. Most of these are small in size, averaging just above 1.5 cm in diameter. We are reporting a case of congenital giant pigmented nevus in a neonate with sacral sinus.