Congenital extracranial extrarenal rhabdoid tumor: A rare clinicopathologic entity and diagnostic challenge

Antonis Kattamis,Kleoniki Roka

doi:10.5348/100069z10ht2020cr

Abstract

Introduction: Extrarenal extracranial rhabdoid tumor (EERT) is a rare tumor characterized by highly aggressive behavior. It is mainly observed in infants and young children.

Highlights

Extrarenal extracranial rhabdoid tumor (EERT) is a rare tumor characterized by highly aggressive behavior
Congenital EERT is a very rare, aggressive entity, with dismal prognosis especially when it develops in a patient with a cancer predisposition syndrome
Diagnosis and genetic evaluation are essential for proper management and genetic counseling

Summary

Conclusion

Congenital EERT is a very rare, aggressive entity, with dismal prognosis especially when it develops in a patient with a cancer predisposition syndrome.

INTRODUCTION

Findings

DISCUSSION

CONCLUSION