Congenital duodenal atresia with ‘apple-peel configuration’ of the small intestines and absent superior mesenteric artery: A case report and review of literature

Abstract

Embryo logically, congenital duodenal atresia is a primary malformation that results from errors in recanalization of the duodenum in early gestation. This is in contrast to other intestinal atresias which result from vascular accidents. We report an unusual and rare case of congenital duodenal atresia, loss of the third and fourth parts of the duodenum with apple-peel configuration of remaining small bowel and absent superior mesenteric artery in a preterm child. The possibility of Strømme syndrome must also be kept in mind. The literature on the subject is also reviewed.