Congenital Constriction Band With Lymphedema in a Neonate: A 17-Year Follow-Up After Single Stage Excision and Z-Plasty.

Levin Kesu Belani,Sharaf Ibrahim,Muhd Kamal Muhd Abdul Jamil,Abdul Halim Abd Rashid,Ahmad Fazly Abd Rasid

doi:10.7759/cureus.15026

Levin Kesu Belani, Sharaf Ibrahim + Show 3 more

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https://doi.org/10.7759/cureus.15026

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Abstract

Congenital constriction band syndrome is a rare condition that presents with constriction bands affecting different types of extremities. Timely surgical intervention for moderate and severe stages of this condition can be performed either in a single stage or multiple stages. We report the case of a neonate who presented with a congenital constriction band and had excision of the constriction band and z-plasty reconstruction. The surgery was done in a single stage. This case highlights the outcome and safety of this single-stage surgery with Z-plasty reconstruction. At 17 years of age, he has a functional lower limb and excels in archery.

Highlights

Congenital constriction band is a condition that can potentially be limb-threatening
A neonate was referred to our tertiary hospital at 14 days after birth with congenital constriction bands of the lower limb
At one year of age, the distal constriction band was excised and the skin reconstructed via z-plasty technique

Summary

Introduction

Congenital constriction band is a condition that can potentially be limb-threatening. A neonate was referred to our tertiary hospital at 14 days after birth with congenital constriction bands of the lower limb. Physical examination revealed an oedematous right lower limb and 2 constriction bands over the leg (Figure 1A,1B). How to cite this article Kesu Belani L, Abd Rashid A, Ibrahim S, et al (May 14, 2021) Congenital Constriction Band With Lymphedema in a Neonate: A 17-Year Follow-Up After Single Stage Excision and Z-Plasty. An emergency single-stage excision of the proximal constriction band including the underlying deep fascia was done(Figure 2A). At one year of age, the distal constriction band was excised and the skin reconstructed via z-plasty technique. Follow-up at two years of age revealed well-healed scars and resolution of the leg oedema (Figure 3). He progressed well and has no limitation of activities of daily living during the latest follow up at age 17 years (Figure 4) and excels in competitive archery

Discussion

Disclosures

Findings

Rayan GM