Abstract
Introduction: Congenital constriction band syndrome (CCBS) or amniotic band syndrome is a complex set of congenital malformations, mainly affecting the limbs, but also the craniofacial and thoraco-abdominal region. The Patients: The purpose of this work is to describe the clinical and diagnostic aspects of CCBS in Togo in relation to 03 clinical cases. The Primary Diagnoses, Interventions, and Outcomes: The first case is characterized by an asymmetric bilateral superficial constriction groove of the lower limbs, pseudosyndactylias and synostosis of the tibia and fibula on X-ray. The second has a deep strangulation in the left arm with an amputation of the fingers associated with hypochromic skin lesions, poorly hemmed polylobal ear and skin growths. The latter characterized by persistent bridle, strangulation and ischemia downstream of that of the left wrist with postnatal amputation of the left hand. Conclusion: The strengthening of antenatal diagnosis, the introduction of genetic counselling and the establishment of a national malformations register should make it possible to improve the management of cases of amniotic flange disease.
Highlights
Congenital constriction band syndrome (CCBS) or amniotic band syndrome is a complex set of congenital malformations, mainly affecting the limbs, and the craniofacial and thoraco-abdominal region
We report a series of three observations on CCBS discovered in three different regions of Togo
In Togo, the cases of CCBS that we report are the first to our knowledge
Summary
Congenital constriction band syndrome (CCBS) or amniotic band syndrome is a complex set of congenital malformations, mainly affecting the limbs, and the craniofacial and thoraco-abdominal region. Congenital constriction band syndrome (CCBS) or amniotic band disease (ABD) is a group of complex congenital malformations, mainly involving the limbs, and the craniofacial region and the thoracoabdominal axis [1]. It includes a group of lesions whose appearance seems to result from the ligation or compression of normal fetal structures: stricture grooves, amputations, pseudosyndactylies, atypical facial clefts, exencephaly. None of these has yet been formally proven in humans
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