Congenital Biliary Tract Dilatation in Children : 13 Years Experience in the Children National Health Institute, Lima, Peru

Abstract

Congenital biliary tract dilatation in the pediatric population is a very rare condition. The signs and symptoms are jaundice, abdominal pain, fever, abdominal mass, sepsis. The frequency in the American population is 1/15,000 and in Japan is 1/1,000. It is more frequent in women and during the neonatal period. 2/3 parts of the CBTD present in children less than 10 years old. No etiology has been identified, the afectation of the embrionary primordium has been postulated, as well as the abnormal union of the choledoco with the pancreatic duct. There are different anatomic forms that include intra and extra hepatic compromise (Todani Classification).