Cone Reconstruction with Successful One and A Half Ventricle Repair for Ebstein Anomaly

Abstract

Ebstein anomaly is a rare pathology among congenital cardiac diseases with a prevalance of 0.5%. Ebstein anomaly patients suffer from arrhytmia, severe right ventricular dysfunction and left ventricular dysfunction due to cyanosis and right ventricular involvement. Most of the patients are presented at infancy, childhood and rarely after adolescence ages. Biventricular repair has a high mortality and morbidity and unacceptable func- tional results in Ebstein anomaly patients with severe right ventricular dysfunction, one and a half ventricle repair yields better results. In our case, we presented a one and a half ventricle repair with a successful Cone type repair in a 34-year-old male patient who referred to our clinic with cardiac arrest presentation and was detected to have functional type C Ebstein anomaly.