Abstract
Pulmonary alveolar microlithiasis (PAM) is a rare lung disease with poor prognosis. The only effective treatment to date, is lung transplantation in the severest cases. However, the etiology of PAM has been recently deciphered, and the treatment paradigm is shifting. We report a case of PAM and propose an optimized imaging-guided management based on the current state of the art.
Highlights
Pulmonary alveolar microlithiasis (PAM) is a rare lung disease with poor prognosis
PAM is a rare autosomal recessive genetic disease characterized by widespread deposits of intra-alveolar minute calcium called microliths or calcospherites without disturbances in calcium and phosphorus metabolism [1]
The evaluation of the kinetics of microliths deposit can be performed with CT-scan, 18F-FDG PET/CT and bone SPECT/CT
Summary
Pulmonary alveolar microlithiasis (PAM) is a rare lung disease with poor prognosis. The only effective treatment to date, is lung transplantation in the severest cases. Comprehensive Imaging-Guided Optimization of the Surgical Management of Patients with Pulmonary Alveolar Microlithiasis Pulmonary alveolar microlithiasis (PAM) is a rare lung disease with poor prognosis. We report a case of PAM and propose an optimized imaging-guided management based on the current state of the art.
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