Complex Infantile Scimitar Variant: Primary Stenosis of a Meandering Pulmonary Vein

Abstract

A 5-month-old girl presented with failure to thrive, pulmonary hypertension, and a meandering intraparenchymal right pulmonary vein (PV), which continued as a confluence of the right upper and lower pulmonary veins (Figure 1, yellow), crossing the midline, and draining into the left atrium with a discrete stenosis at the connection. 1 Tsitouridis I. Tsinoglou K. Morichovitou A. et al. scimitar syndrome versus meandering pulmonary vein: evaluation with three-dimensional computed tomography. Acta Radiol. 2006; 47: 927-932 Crossref PubMed Scopus (15) Google Scholar ,2 Dupuis C. Charaf L.A.C. Breviere G.M. et al. Infantile form of the scimitar syndrome with pulmonary hypertension. Am J Cardiol. 1993; 71 (1326-1230) Abstract Full Text PDF Scopus (110) Google Scholar Adjacent was a stenotic left lower PV (Figure 1, red). The left upper PV was normal in caliber and position (Figure 1, blue).