Common pulmonary vein atresia.

Thomas Glenn,Dana Mueller,Jose Honold,Beth F Printz

doi:10.1017/s1047951121003565

Abstract

A 4-hour-old infant with profound cyanosis on an alprostadil infusion was urgently transferred to Rady Children's Hospital with suspected CHD. Upon arrival, urgent echocardiography was performed but could not confirm the presence of discrete pulmonary veins or pulmonary venous drainage. Given the difficulty in delineating the anatomy, a cardiac CT scan was performed and demonstrated a nearly atretic common pulmonary vein with multiple small collaterals that drained to systemic veins. Due to the high risk of mortality associated with operative repair, the decision was made to proceed with compassionate withdrawal of care. The described anatomy of common pulmonary vein atresia remains rare, and to our knowledge, fewer than 40 cases have been reported in the literature. Albeit rare, common pulmonary vein atresia should be considered in the differential diagnosis of a severely cyanotic neonate.

Highlights

A newborn female was born at 39 3/7 weeks gestational age at an outside hospital to a 32-yearold G2P0 Hawaiian female with adequate prenatal care
The described anatomy of common pulmonary vein atresia remains rare, and to our knowledge, fewer than 40 cases have been reported in the literature
Given that discrete pulmonary veins or venous drainage could not be delineated by echocardiography, cardiac CT scan was emergently obtained

Summary

Introduction

A newborn female was born at 39 3/7 weeks gestational age at an outside hospital to a 32-yearold G2P0 Hawaiian female with adequate prenatal care. The described anatomy of common pulmonary vein atresia remains rare, and to our knowledge, fewer than 40 cases have been reported in the literature.

Results

Conclusion