Abstract
We describe the management of the congenital entropion with tarsal kink in a case of mobius syndrome. Mobius syndrome is extremely rare congenital neurological disorder results from the underdevelopment of the sixth and seventh cranial nerves which causes facial paralysis and inability to move the eyes from side to side. A congenital malformation of the tarsus known as tarsal kink was the associated eyelid anomaly which caused upperlid entropion. A two year old girl presented with both eyelids entropion of left eye which was corrected by upper lid tarsotomy, marginal rotation and levator suturing with tarsal plate and lower lid retractors were strengthened by their advancement to the tarsal plate.
Highlights
The tarsal kink syndrome (TKS), a rare and severe form of congenital upper eyelid entropion with a marked kink in the entire horizontal length of the upper tarsal plate with resultant inversion of the eyelid margin, was described in 1948.1The etiology of tarsal kink may be attributed to overacting orbicularis fibers, an aponeurotic defect, a primary tarsal defect or an exogenous mechanical force in utero.[2]
We report a case of unilateral TKS of the upper eyelid and entropion of both lids in a case of Möbius syndrome (MS) which has not been reported in literature yet
MS is a rare condition characterized by sixth and seventh nerve palsies. It is often diagnosed later, it can be recognized in infants with ‘mask-like’ expressionless facies noticed during crying and by an inability to suck while nursing because of seventh cranial nerve palsy
Summary
The tarsal kink syndrome (TKS), a rare and severe form of congenital upper eyelid entropion with a marked kink in the entire horizontal length of the upper tarsal plate with resultant inversion of the eyelid margin, was described in 1948.1The etiology of tarsal kink may be attributed to overacting orbicularis fibers, an aponeurotic defect, a primary tarsal defect or an exogenous mechanical force in utero.[2]. The tarsal kink syndrome (TKS), a rare and severe form of congenital upper eyelid entropion with a marked kink in the entire horizontal length of the upper tarsal plate with resultant inversion of the eyelid margin, was described in 1948.1 A two-year-old girl presented with tearing from left eye since birth and found to have inturned lashes in both upper and lower lids.
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