Abstract
Background: Colonic atresia (CA) is a rare form of congenital intestinal atresia. Although CA may be isolated, it is more commonly reported in literature in association with other congenital anomalies. Materials and Methods: This study is a review of prospectively collected data of all the patients with colonic atresia presented to our center (Ain Shams University) during 2008 to 2016. Results: Twelve patients were enrolled in this study. The atresia was of type I in one case, type II in four cases, type IIIa in six cases, type IV in one case. These cases accounted for 4.9 % of intestinal atresias managed in our center during the same period. Five cases were isolated CA, while the other seven cases had associated abdominal congenital anomalies (exomphalos, Hirschsprung's disease, imperforate anus, closing gastroschisis, colonic duplication, and multiple small bowel atresia in two cases). The management in ten cases was by staged procedure with creation of a temporary stoma initially, while primary anastomosis was established in two cases. We had two cases with delayed presentations, one missed diagnosis, and three mortalities in this series. Conclusions: The low incidence of CA may result in delay in the diagnosis and management. Hirschsprung's disease should be excluded in every case of colonic atresia. Early diagnosis and proper surgical management is essential for good prognosis.
Highlights
Colonic atresia (CA) is a rare cause of congenital intestinal obstruction with a reported incidence of approximately 1:66,000 live births [1]
These cases accounted for 4.9 % of intestinal atresias managed in our center during the same period
The management in ten cases was by staged procedure with creation of a temporary stoma initially, while primary anastomosis was established in two cases
Summary
Colonic atresia (CA) is a rare cause of congenital intestinal obstruction with a reported incidence of approximately 1:66,000 live births [1]. Since it is a rare condition, CA represents a challenge for the pediatric surgeons regarding its diagnosis and management. Associated anomalies vary between abdominal anomalies (abdominal wall defect, multiple intestinal atresia, Hirschsprung’s disease, and malrotation) and extra abdominal anomalies (musculoskeletal, ocular, and facial anomalies) [2] Among these anomalies, the presence of associated Hirschsprung’s disease represents a main issue in surgical decision making whether to do a primary anastomosis or to fashion a temporary stoma. CA may be isolated, it is more commonly reported in literature in association with other congenital anomalies
Sign-in/Register to view highlights & summary Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a callDisclaimer: All third-party content on this website/platform is and will remain the property of their respective owners and is provided on "as is" basis without any warranties, express or implied. Use of third-party content does not indicate any affiliation, sponsorship with or endorsement by them. Any references to third-party content is to identify the corresponding services and shall be considered fair use under The CopyrightLaw.
