Abstract

SMARCA4缺失性肿瘤是一组少见的高侵袭性肿瘤,因缺乏特异性分化易被误诊。提高对这一组新病种的认识不仅有助于诊断和鉴别诊断,也可为临床治疗和预后判断提供重要信息。本文对各系统SMARCA4缺失性肿瘤加以总结,介绍其临床病理学特征、免疫表型及鉴别诊断。.

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