Clinical features and treatment of the hemorrhagic moyamoya disease

Abstract

Objective To study the clinical features, bleeding reasons and strategies of the treatment of 61 patients with hemorrhagic moyamoya disease. Method The clinical features of onset, bleeding location of the lesions and the type, characteristics of DSA images and therapeutic results were studied retrospectively. Results In all 61 patients, 57 patients were adult. Most of them were cerebral hemorrhage breaking into ventricles. In all the hemisphere of hemorrhage, dilatation and abnormal branching of the AChA and P-CoM were observed in 52 patients. 118 procedures of EDAS were performed,including superficial temporal artery in 116 hemispheres and occipital artery in 2 hemispheres. There was no recurrence of hemorrhage in those operation patients. But 2 patients without EDAS died due to recurrence of hemorrhage. Conclusions Dilatation and abnormal branching of the AChA and/or P - CoM are one of the main reasons for hemorrhagic events. The treatment of EDAS may be an effective method for preventing the recurrence of hemorrhage of hemorrhagic moyamoya disease. Key words: Moyamoya disease; Cerebral hemorrhage; Cerebroventricular haemorrhage