Abstract
Retiform hemangioendothelioma (RH) is an uncommon vascular neoplasm of borderline malignancy that clinically develops as a solitary, gradually enlarging exophytic mass, nodule or plaque, most often on the lower limbs, upper limbs and trunk. Clinical recognition of RH is troublesome because of its non-specific appearance, with differential diagnosis comprising a variety of benign and malignant tumors clinically presenting as reddish nodules. In this article we describe the clinical, dermoscopic and histopathologic findings in a case of RH developing on the flank of a 26-year-old woman, and discuss the possible role of dermoscopy in facilitating the clinical recognition of this rare tumor.
Highlights
Hemangioendothelioma is a term encompassing neoplasms with an intermediate biological behavior between benign hemangiomas and angiosarcomas
Clinical recognition of Retiform hemangioendothelioma (RH) is troublesome because of its non-specific appearance, with differential diagnosis comprising a variety of benign and malignant tumors clinically presenting as reddish nodules
In this article we describe the clinical, dermoscopic and histopathologic findings in a case of RH developing on the flank of a 26-year-old woman, and discuss the possible role of dermoscopy in facilitating the clinical recognition of this rare tumor
Summary
Hemangioendothelioma is a term encompassing neoplasms with an intermediate biological behavior between benign hemangiomas and angiosarcomas. It affects the skin and the soft tissues and includes retiform hemangioendothelioma (RH), papillary intralymphatic angioendothelioma (PILA, Dabska’s tumor), epithelioid, kaposiform, pseudomyogenic, and composite hemangioendotheliomas [1]. RH typically develops as a solitary, gradually enlarging exophytic mass, nodule or plaque, most often on the lower limbs, upper limbs and trunk. A case of RH presenting with multiple lesions on the limbs and trunk has been described [3]. Surgical excision is the treatment of choice for RH [1,2,3,4]. Accurately defining the excision margins in a vascu-. Regional lymph node metastasis was reported in a single patient, while no distant metastases have been reported to date [4]
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