Abstract
Classic case of cleidocranial dysplasia with an infected mandibular cyst
Highlights
Cleidocranial dysplasia, is a congenital disorder of bone formation with prominent manifestations being clavicular hypoplasia/agenesis with a narrow thorax, delayed ossification of skull bones, excessively large fontanelles and delayed closing of sutures [1]
Marie and Sainton in 1897 used the term cleidocranial dysostosis [3]. It has since been known as cleidocranial dysplasia in recognition of its underlying pathology being more of a generalized skeletal dysplastic condition
Zheng et al reported that humans with cleidocranial dysplasia have altered
Summary
Cleidocranial dysplasia, is a congenital disorder of bone formation with prominent manifestations being clavicular hypoplasia/agenesis with a narrow thorax, delayed ossification of skull bones, excessively large fontanelles and delayed closing of sutures [1]. We present a case report of a patient with classical features of cleidocranial dysplasia with symptomatic infected mandibular cyst probably secondary to multiple impacted teeth and its management with surgical enucleation and debridement. The panoramic radiograph on examination revealed a diffuse radiolucency in the area of interest suggestive of excessive bone loss due to the cystic lesion along with multiple impacted teeth (around 24 in number) and non-prominent gonial angle bilaterally (Figure 3). A surgical treatment plan involving surgical enucleation and debridement of affected tissue and disimpaction of multiple involved impacted teeth in the area of concern under general anesthesia with supportive systemic antibiotics and Figure 1: Intraoral views: (A) Right lateral, (B) Left lateral, (C) Frontal
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