Chordoid glioma: a rare suprasellar mass

Abstract

Chordoid glioma is a relatively new entity since the histopathology of a series of low-grade tumors arising in the area of the hypothalamus and the anterior third ventricle was first described in 1998 [1]. The characteristic histopathology shows features of a chordoma as well as positive staining for glial fibrillary acidic protein (GFAP) favoring a glial derivation. Therefore, the tumor was named a ‘‘chordoid glioma’’. An evaluation of the imaging studies of these patients showed a remarkable resemblance, creating the potential to suggest the diagnosis prospectively based on MR imaging.