Childhood spinal extradural EWING'S sarcoma: A case report

Abstract

Extraosseous, extradural and extramedullary Ewing's sarcoma is a rare tumor that usually affects young people. We report a 10 years old child operated for Inguinal Hernia at the age of 4 years which presents a lumbar spinal syndrome for 4 months, the second is a 3 years old child with a history of falls on stairs 4 months ago, presented for 14 days before his admission a right leg paresis at ⅗ on the muscular testing, associated with fever. Both patients underwent magnetic resonance imaging that showed a compressive extradural process from L2 to L5 for the first case and a compressive extradural process from L4 to S2 for the second case. The patients benefited from macroscopic total resection by laminectomy. Histology confirms the diagnosis of Ewing’s Sarcoma. Both patients were referred at discharge to the pediatric oncology department for complementary chemotherapy management. The long-term follow-up at three years was good clinically with no recurrence on imaging. Spinal Ewing’s Sarcoma extradural without bone involvement remains rare and its overall survival at 5 years is still poor.