Childhood Onset Erythrokeratoderma En Cocardes Treated with Oral Acitretin

Abstract

Erythrokeratoderma are genodermatose of keratinisation which usually presents in infancy. Erythrokeratoderma en cocardes is a rare variant of erythrokeratoderma which presents as polycyclic hyperkeratotic plaques with a peripheral desquamation, forming a concentric appearance termed ‘en cocarde’. Here, we report a case of erythrokeratoderma en cocardes with onset in childhood showing excellent response after 2 months of acitretin therapy.