Abstract
BackgroundCongenital infantile fibrosarcoma is a rare mesenchymal tumor seen in children as well as adults. The congenital variety is rare and out of the reported cases only one case sited in the neck has been reported so far. Another such case is presented here who was successfully managed.Case presentationA 3-month-old Hindu baby boy presented with a congenital neck swelling. The apparent clinical diagnosis was lympho-venous malformation. With a remote possibility of malignancy, an excisional biopsy was done. Histopathology revealed congenital infantile fibrosarcoma.ConclusionA successful excision of cervical congenital infantile fibrosarcoma has not been reported. This diagnosis should be kept as a possibility in all congenital cervical swellings. These are commonly misdiagnosed as lympho-venous malformations and histopathology is confirmatory.
Highlights
Congenital infantile fibrosarcoma is a rare mesenchymal tumor seen in children as well as adults
Case presentation A 3-month-old Hindu baby boy presented with a congenital neck swelling on the right side of his neck
The congenital and adult types of infantile fibrosarcoma, histologically similar, differ in their clinical presentation in that the adult type has a higher risk of recurrence, higher incidence of metastasis, and fairs poorly in the overall survival
Summary
Congenital infantile fibrosarcoma is a rare mesenchymal tumor seen in children as well as adults. Background Congenital infantile fibrosarcoma (CIFS) is a rare mesenchymal tumor which, contrary to its name, is seen both in children as well as adults. * Correspondence: drshilpas@gmail.com 1Department of Pediatric Surgery, All India Institute of Medical Sciences, New Delhi, India Full list of author information is available at the end of the article month after the bleomycin injection, it was a 5.5 × 7.5 cm firm, non-tender, well-defined swelling in the midline and extending into the right supraclavicular region (Fig. 1).
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